A case of primary idiopathic cutaneous pustular vasculitis.

© 2010 The Authors. doi: 10.2340/00015555-0857 Journal Compilation © 2010 Acta Dermato-Venereologica. ISSN 0001-5555 Primary idiopathic cutaneous pustular vasculitis (PICPV) is a rare clinical entity, which was first reported by McNeely et al. in 1986 (1). The disease is characterized by tender, purpuric pustules that recur several times over a period of 3–4 months, histological findings of Sweet’s-like vasculitis, the presence of circulating immune complexes, deposit of immune complex in blood vessels, and the absence of other diseases associated with pustular lesions. We report here a second case with clinical manifestations compatible with this disease.